Auditory processing is impaired in Charcot-Marie-Tooth disease despite normal audiograms

Takeaway

  • People with Charcot-Marie-Tooth disease types 1A and 2A can have normal audiograms but impaired auditory processing.

Why this matters

    These novel findings highlight that people with Charcot-Marie-Tooth disease, who complain of hearing loss despite normal audiograms, have difficulty perceiving speech in noisy backgrounds. This distinctive auditory dysfunction should be considered when deciding on hearing aid signal processing to assist hearing rehabilitation.